<?xml version="1.0" encoding="UTF-8"?>
<protein>
  <version>1.0</version>
  <creation_date>2018-05-07 22:26:20 UTC</creation_date>
  <update_date>2020-05-20 22:25:41 UTC</update_date>
  <accession>BMDBP01298</accession>
  <secondary_accessions>
  </secondary_accessions>
  <protein_type>Enzyme</protein_type>
  <synonyms>
  </synonyms>
  <gene_name>B4GAT1</gene_name>
  <general_function>Involved in N-acetyllactosaminide beta-1,3-N-acetylgluc</general_function>
  <specific_function>Beta-1,4-glucuronyltransferase involved in O-mannosylation of alpha-dystroglycan (DAG1). Transfers a glucuronic acid (GlcA) residue onto a xylose (Xyl) acceptor to produce the glucuronyl-beta-1,4-xylose-beta disaccharide primer, which is further elongated by LARGE1, during synthesis of phosphorylated O-mannosyl glycan. Phosphorylated O-mannosyl glycan is a carbohydrate is a carbohydrate structure present in alpha-dystroglycan (DAG1), which is required for binding laminin G-like domain-containing extracellular proteins with high affinity. Required for axon guidance; via its function in O-mannosylation of alpha-dystroglycan (DAG1).</specific_function>
  <pathways>
    <pathway>
      <name>Protein glycosylation</name>
      <smpdb_id/>
      <kegg_map_id/>
    </pathway>
    <pathway>
      <name>Protein modification</name>
      <smpdb_id/>
      <kegg_map_id/>
    </pathway>
  </pathways>
  <metabolite_associations>
    <metabolite>
      <accession>BMDB0000290</accession>
      <name>Uridine diphosphate-N-acetylglucosamine</name>
    </metabolite>
  </metabolite_associations>
  <go_classifications>
  </go_classifications>
  <subcellular_locations>
  </subcellular_locations>
  <gene_properties>
    <chromosome_location>29</chromosome_location>
    <locus/>
    <gene_sequence>&gt;1248 bp
ATGCAGATGTCCTACGCCATCCGATGTGCCTTCTACCAGCTGCTGCTGGCCGCGCTCATG
CTGGTGGCTATGCTGCAGCTGCTCTACCTGTCGCTGCTGTCCGGGCTGCATGGGCAAGAA
GAGCAAGACCAATATTTCGAGTTCTTTCCCCCATCCCCGCGGTCGGTGGACCAAGTCAAG
GCGCAGCTCCGCACCGCGCTGGCCTCCGGAGGCGTCCTGGACGCCAGCGGCGACTACCGC
GTCTACAGGGGCCTACTGAAGACCACCATGGACCCCAACGATGTGATCCTGGCCACTCAC
GCCAGTGTGGACAACCTGCTGCACCTGTCGGGCCTGTTGGAGCGCTGGGAGGGCCCTCTG
TCGGTGTCGGTGTTCGCCGCCACCAAGGAGGAGGCGCAGCTGGCCACGGTGCTGACCTAC
GCGCTGAGCAGCCACTGCCCCGATATGCGTGCCAGGGTCGCCATGCACCTTGTGTGCCCC
TCACGCTACGAGGCCGCCGTTCCCGACCCCCGGGAGCCAGGGGAGTTTGCCCCGTTGCGT
TCCTGCCAGGAGGTCTTTGACAAGCTGGCTAGGGTGGCCCAGCCCGGGGTCAATTACGCG
CTGGGCACCAACGTCTCCTACCCCAATAACCTGCTGAGGAATCTGGCTCGTGAGGGGGCC
AACTATGCCCTGGTAATCGACGTGGACATGGTGCCCAGCGAGGGGCTGTGGAGAAGCCTG
CGGGAAATGCTGGATCAGAGCAAGCAGTGGGCGGGCACAGCGCTGGTGGTGCCTGCCTTT
GAGATCCGTCGAGCTCGCCGCATGCCCATGAACAAAAACGAGCTGCTGCAGCTCTACCAG
GTGGGCGAGGTGCGGCCCTTCTATTATGGGCTCTGCACCCCCTGCCAGGCGCCCACCAAC
TACTCCCGCTGGGTCAACCTGCCAGAAGAGACCTTGCTGAGGCCTGCCTACGTGGTGCCC
TGGCAAGACCCCTGGGAGCCATTCTACGTGGCTGGAGGCAAGGTGCCCACCTTCGACGAG
CGCTTTCGGCAGTATGGCTTCAATCGTATCAGCCAGGCCTGTGAGCTGCACGTGGCAGGA
TTCGATTTCGAGGTGCTGAATGAAGGTTTCCTGGTTCATAAAGGCTTCAAAGAAGTTTTG
AAATTCCATCCCCAAAAGGAGGCTGAAAATCAGCACAATAAGATCCTTTACCGTCAGTTC
AAACAGGAGTTGAAGGCCAAGTACCCTGACTCCCCGCGTCACTGCTGA</gene_sequence>
  </gene_properties>
  <protein_properties>
    <residue_number>415</residue_number>
    <molecular_weight>47231.0</molecular_weight>
    <theoretical_pi>7.03</theoretical_pi>
    <pfams>
    </pfams>
    <transmembrane_regions>
      <region>9-36</region>
    </transmembrane_regions>
    <signal_regions>
      <region>None</region>
    </signal_regions>
    <polypeptide_sequence>&gt;N-acetyllactosaminide beta-1,3-N-acetylglucosaminyltransferase
MQMSYAIRCAFYQLLLAALMLVAMLQLLYLSLLSGLHGQEEQDQYFEFFPPSPRSVDQVK
AQLRTALASGGVLDASGDYRVYRGLLKTTMDPNDVILATHASVDNLLHLSGLLERWEGPL
SVSVFAATKEEAQLATVLTYALSSHCPDMRARVAMHLVCPSRYEAAVPDPREPGEFALLR
SCQEVFDKLARVAQPGVNYALGTNVSYPNNLLRNLAREGANYALVIDVDMVPSEGLWRSL
REMLDQSKQWAGTALVVPAFEIRRARRMPMNKNELLQLYQVGEVRPFYYGLCTPCQAPTN
YSRWVNLPEETLLRPAYVVPWQDPWEPFYVAGGKVPTFDERFRQYGFNRISQACELHVAG
FDFEVLNEGFLVHKGFKEVLKFHPQKEAENQHNKILYRQFKQELKAKYPDSPRHC</polypeptide_sequence>
  </protein_properties>
  <genbank_protein_id>AAX08785.1</genbank_protein_id>
  <uniprot_id>Q5EA01</uniprot_id>
  <uniprot_name>B4GA1_BOVIN</uniprot_name>
  <pdb_ids>
  </pdb_ids>
  <genbank_gene_id>BT020768</genbank_gene_id>
  <genecard_id>B4GAT1</genecard_id>
  <geneatlas_id/>
  <general_references>
  </general_references>
  <metabolite_references>
  </metabolite_references>
</protein>
